Recurrent Shoulder Dislocation and Proximal Humerus Fracture in Neurofibromatosis Type I: A Case Report

Hwang,  Tae Hyok; Cho,  Hyung Lae; Wang,  Tae Hyun; Yang,  Hui Sun

doi:2013.16.2.135

Clin Shoulder Elb > Volume 16(2); 2013 > Article

Case Report

Clinics in Shoulder and Elbow 2013;16(2):135-140.
DOI: https://doi.org/10.5397/CiSE.2013.16.2.135 Published online December 31, 2013.

Recurrent Shoulder Dislocation and Proximal Humerus Fracture in Neurofibromatosis Type I: A Case Report

Tae Hyok Hwang, Hyung Lae Cho, Tae Hyun Wang, Hui Sun Yang

Department of Orthopaedic Surgery, Good Samsun Hospital, Busan, Korea. toocoolyo@naver.com

제 1형 신경 섬유종증 환자에서 발생한 재발성 견관절 탈구 및 근위 상완골 골절 - 1예 보고 -

황태혁·조형래·왕태현·양희순

좋은삼선병원 정형외과

Abstract

We report a case of recurrent shoulder dislocation and combined proximal humerus fracture in neurofibromatosis type I. A twenty-year-old male patient with known neurofibromatosis type I presented with right shoulder dislocation and proximal humerus fracture following a minor trauma. His injured arm also had large plexiform neurofibromas on the elbow, and the dislocation of the shoulder joint was proven to be recurrent. Bony deformation of the humerus and scapula were revealed on X-ray and computed tomography, as well as multiple neurofibromatic changes of the deltoid and periscapular muscles were noted on magnetic resonance imaging. Open reduction and capsular reconstruction were performed and humeral fracture was stabilized with a reconstruction plate. Satisfactory union and functional result were achieved and the dislocation did not recur until the 7-month follow-up after the procedure. Recurrent shoulder dislocation and combined proximal humerus fracture in neurofibromatosis type I are rare complications. However, it should still be considered in the orthopaedic evaluation process of the diseases.

Key Words: Neurofibromatosis type I; Recurrent shoulder dislocation; Proximal humerus fracture